How does Klippel-Trenaunay Syndrome affect the circulatory system?
Varicose veins can cause pain and skin ulcers due to poor circulation. Deeper malformed veins can increase the risk of blood clots (deep vein thrombosis) and cause a life-threatening condition called pulmonary embolism if the clots dislodge and travel to the lungs.
What is the lateral marginal vein?
The lateral marginal vein (also known as the vein of Servelle or the Klippel-Trenaunay vein) is one of two known persisting embryonic veins of the leg, the persistent sciatic vein being the other.
Is Klippel-Trenaunay Weber syndrome a disability?
If you or your dependent(s) are diagnosed with Klippel-Trenaunay Syndrome and experience any of these symptoms, you may be eligible for disability benefits from the U.S. Social Security Administration.
Is Klippel-Trenaunay Syndrome painful?
The abnormal growth can cause pain, a feeling of heaviness, and reduced movement in the affected area. If the overgrowth causes one leg to be longer than the other, it can also lead to problems with walking. Malformations of veins are the third major feature of Klippel-Trenaunay syndrome.
Is KTS life-threatening?
KTS is often a progressive disorder, and complications may be life-threatening. However, many individuals can live well while managing their symptoms. KTS is often a progressive disorder, and complications may be life-threatening. However, many individuals can live well while managing their symptoms.
How do you test for Klippel-Trenaunay?
Some tests include:
- Duplex ultrasound scanning. This test uses high-frequency sound waves to create detailed images of blood vessels and blood flow.
- MRI and magnetic resonance (MR) angiography.
- Scanogram.
- CT scan or CT angiography.
- Contrast venography.
- Coagulation studies.
- Genetic studies.
What is the great cardiac vein?
The great cardiac vein (GCV) runs in the anterior interventricular groove and drains the anterior aspect of the heart where it is the venous complement of the left anterior descending artery. It is the main tributary of the coronary sinus.
Where is the marginal vein?
The right marginal vein is a small vein that drains blood from the heart. It passes along the inferior margin of the heart and joins the small cardiac vein (sometimes known as the right coronary vein) in the coronary sulcus, or opens directly into the right atrium.
Can Klippel-Trenaunay be treated?
There is no cure for KTS. Treatment is symptomatic. Laser surgery can diminish or erase some skin lesions. Surgery may correct discrepancies in limb size, but orthopedic devices may be more appropriate.
Is Klippel-Trenaunay life threatening?
Klippel-Trenaunay syndrome (KTS) is a rare congenital syndrome of vascular malformations and soft tissue and bone hypertrophy. Vascular malformations can affect multiple organ systems. Involvement of the gastrointestinal (GI) tract is uncommon in KTS, but it can be a source of life-threatening bleeding.
Is there a cure for Klippel-Trenaunay?
How is Klippel-Trenaunay diagnosed?
Diagnosis of Klippel-Trenaunay syndrome begins with a physical exam. Referral to a vascular malformations specialist is helpful for evaluation and treatment recommendations.